Duplicación esofágica: caso clínico / Esophageal duplication: a case report

We report an 11-month infant case, who consults electively to perform a laparoscopic Nissen fundoplication, given her background of gastro-esophageal reflux and hiatal hernia. Intraoperatively, a malformation of the distal third of the esophagus was found. The preoperative images showed no evidence of the lesión. The lesión was resected and sent to anatomopathologic analysis, confirming the diagnosis.

Se presenta el caso de una lactante de 11 meses con antecedentes de reflujo gastroesofágico y hernia hiatal que ingresa electivamente a la Sección de Cirugía Pediátrica, con el objetivo de realizar una fundoplicatura de Nissen laparoscópica. En el intraoperatorio se detecta una malformación en el tercio distal del esófago. En las imágenes realizadas previamente no se observó una alteración compatible. La lesión fue resecada y luego analizada en anatomía patológica, confirmándose el diagnóstico de una duplicación esofágica.

Complex Bronchopulmonary Foregut Malformation: Extralobar Pulmonary Sequestration Communicating with an Esophageal Duplication Cyst: A Case Report

We report here on a case of a rare, complex bronchopulmonary foregut malformation (BPFM) that was composed of an extralobar pulmonary sequestration communicating with an esophageal duplication cyst. A 33-year-old female presented with an incidentally detected chest mass. The computed tomography revealed a 7.5 x 4.0 cm sized heterogeneous, solid and cystic lesion in the right superior mediastinum. Surgical resection demonstrated the solid portion to be isolated lung tissue invested in its own pleura. A unilocular cyst was communicating with the bronchus of the sequestrated lung, and microscopically the cyst was lined by squamous epithelium overlying the thick layers of smooth muscle. This case is important for understanding the spectrum of BPFMs and for differentiating a mediastinal mass, especially one at the unusual location.

Obesidad mórbida asociada a quiste broncogénico y leiomioma subcardial que simula GIST: caso clínico / Morbid obesity, esophageal bronchogenic cyst and subcardial leiomioma: report of one case

Gastric wall diseases are found in approximately of 1 percent of the patients submitted to bariatric surgery. Half of these are leiomiomas. Esophageal bronchogenic cysts are exceptional We report a 57 years old female with morbid obesity, a bronchogenic esophageal cyst and subcardial leiomioma. The preoperative study and intraoperative biopsy, suggested the presence of a gastrointestinal stromal tumor (GIST), but the definitive pathological study did not confirm its presence. A total gastrectomy was performed, with an uneventful postoperative course.

La patología intramural gástrica tiene una frecuencia menor al 1 por ciento, en cirugía gástrica. Alrededor del 50 por ciento corresponden a leiomiomas. Los quistes broncogénicos tienen origen embriológico y son excepcionales, y la mayor parte de los reportes corresponden a pacientes pediátricos. Se presenta un caso clínico de paciente portadora de Obesidad mórbida (IMC = 52), asociado a lesión subcardial que simula GIST, cuyo estudio histopatológico resultó ser un quiste esofágico de origen broncogénico de 40 mm, asociado a leiomioma subcardial de 10 mm. Fue sometida a gastrectomía total más anastomosis esófago-yeyunal en Y de Roux, con asa de 180 cm. No presentó morbi-mortalidad postoperatoria. Se discuten los métodos de estudio preoperatorio y las alternativas terapéuticas. No hemos encontrado en la literatura otro caso de asociación de estas raras patologías.

Isolated oesophageal cyst connected with the bronchus

We report an unusual case of a patient with an oesophageal cyst connected to the bronchus. A 24-year old male with a two-year history of repeated attacks of chest infection and haemoptysis was found to have a cyst of 4 x 4 cm affecting the anterior and apical segments of the right upper lobe. The cyst was excised in its entirety and the histopathological study of the cyst showed stratified squamous epithelium with submucosal and muscular layer but no cartilage. The pathological diagnosis was an oesophageal cyst. No previous case of isolated oesophageal cyst connected to the bronchus has been reported according to the available literature.

Unusual Bronchopulmonary Foregut Malformation Associated with Pericardial Defect: Bronchogenic Cyst Communicating with Tubular Esophageal Duplication

We report a case of unusual bronchopulmonary foregut malformation composed of a mediastinal bronchogenic cyst with sequestrated lung tissue and communicating tubular esophageal duplication associated with complete pericardial defect. A 18-yrold man, who had suffered from dry cough and mild dyspnea, was admitted because of an incidentally detected chest mass. A computed tomography scan demonstrated a cystic mass with an air fluid level connected with esophagus in the middle mediastinum. The surgically resected mass was a pleural invested accessory lobe of the lung (8.0x7.0x4.5 cm) connected with the esophageal wall by a tubular structure (3.0 cm in length and 2.0 cm in diameter). A complete left pericardial defect was also identified. Histologically, the cystic wall was composed of fibrovascular connective tissue with a smooth muscle layer, mixed seromucous glands and cartilage, and the inner surface of the cyst was lined by ciliated pseudostratified columnar epithelium. The inner surface of the tubular structure was lined by non-keratinizing or keratinizing squamous epithelium, and the wall contained submucosal mucous glands, muscularis mucosa, and duplicated muscularis propria. This case is important in understanding the embryological pathogenesis of the variable spectrum of the bronchopulmonary foregut malformation.

Intramural Bronchogenic Cyst of the Esophagus: A case report / 대한흉부외과학회지

Bronchogenic cysts are usually located in the pulmonary parenchyma or mediastinum. When they are located in the mediastinum, they are usually near the bronchus or esophagus, but they are rarely at an intramural location of the esophagus. It is very difficult to differentiate between bronchogenic cyst and esophageal cyst before the operation. We report here on a patient for whom the preoperative diagnosis was supposed to be an esophageal cyst. The esophageal cyst was excised through the longitudinal division of the esophageal muscular layer without injury of the mucosa after right thoracotomy. The pathologic report revealed intramural bronchogenic cyst. We report here on a case of bronchogenic cyst that was located in the muscle layer of the lower esophagus.

Quiste entérico de esófago. Tratamiento laparoscópico / Enterogenous cysts of esophagus. Laparoscopic treatment

Los tumores benignos y los quistes del esófago aunque raros, son importantes desde el punto de vista del diagnóstico y de su tratamiento, pues es importante diferenciarlos de la patología maligna. Estos últimos llamados también quistes enterógenos, quistes por duplicación o quistes de inclusión; se originan en la división dorsal del intestino anterior que se convierte en tubo gastrointestinal. En el Hospital Departamental Mario Correa Rengifo de Cali se practicó tratamiento laparoscópico a una paciente con un quiste entérico del esófago; se trataba de una mujer de 20 años de edad con disfagia y pérdida de peso debidos a una obstrucción del esófago distal. Se describe la técnica quirúrgica y se revisa el tema.

Esophageal cyst--a case report.

Mediastinal cysts are rare and classified into thymic cysts, bronchogenic cysts, enteric cysts, pericardial cysts, lymphatic cysts and other rare types. We describe a case of foregut cyst of esophageal type in a 22 day old male infant. The CT scan showed a cystic lesion. Excised cyst was bilocular and was filled with clear fluid. Microscopically, the cyst was lined by columnar epithelium with well formed lamina propria and double layered muscularis. In view of presence of double layer of muscularis and absence of gastric glands, intestinal epithelium or cartilage, it was classified as esophageal cyst. We report this case of esophageal cyst because of its rarity.

Esophageal Duplication Cyst / 대한소화기학회지

No abstract available.

Intra-abdominal Esophageal Duplication Cyst in an Adult

Esophageal duplication cysts are congenital anomalies of the foregut that are rarely found in the abdomen. An accurate preoperative diagnosis is not always possible, so the definitive diagnosis can be made by histologic examination of the surgical specimen. We experienced a case of Intra-abdominal esophageal duplication cyst in a 52-year-old female, who initially presented with an esophageal submucosal tumor on upper gastrointestinal endoscopy. She did not have any gastrointestinal symptoms. Barium esophagography, chest computed tomography scan and endoscopic ultrasonography demonstrated the cystic lesion in the intra-abdominal esophagus. Transhiatal enucleation of the lesion was performed successfully via the abdominal approach with no postoperative complications. Histologic study showed that the cyst wall contained a two-layered muscle coat and the surface of the lumen was lined by pseudo-ciliated columnar epithelium. The patient has been doing well without any complaints for 3 months of follow-up period.

Oesophageal duplication cyst causing neonatal haemoptysis.

Duplication anomalies of the alimentary tract often present with myriad clinical symptoms and signs. There have been no reports of haemoptysis as the presenting feature and oesophageal duplication cyst is not considered as a cause for haemoptysis. An infant presented with this unusual manifestation. Chest X-ray showed persistent right upper zone haziness and contrast enhanced computed tomographic scan showed a multiloculated mass on the right side of the chest. The cystic mass was excised via a right thoracotomy and dense adhesions were noted with the oesophagus. The postoperative period was uneventful and histopathological examination revealed it to be a duplication cyst with ectopic gastric mucosa. Thus, the diagnosis was made retrospectively.

Mediastinal foregut duplication cysts.

Foregut duplication cysts are rare congenital anomalies of enteric origin. In majority of the patients, the diagnosis is made in infancy. The authors report 4 cases of mediastinal foregut duplication cyst in children diagnosed on CT/MRI and confirmed on histopathology. In none of the cases the cysts had intraspinal extension nor heterotopic gastric mucosa.

Infected esophageal duplication cyst simulating empyema.

Duplications of the esophagus are the second most common duplication of the gastrointestinal tract. The children with esophageal duplication cyst usually present with respiratory distress or as asymptomatic thoracic mass found on incidental chest x-ray. We report a case of infected esophageal duplication cyst initially confused with empyema in a two years old boy.

True giant intra-abdominal esophageal cyst.

Isolated intra-abdominal duplication cysts of foregut origin are extremely rare and are discovered incidentally. We report a 70-year-old lady with a giant, truly intra-abdominal esophageal duplication cyst. She was symptom-free one year after excision of the cyst.

Rare intramural bronchogenic cyst of esophagus

Peri-esophageal bronchogenic cysts are well recognised and have been frequently reported in literature. On the contrary, complete intramural bronchogenic cyst of esophagus is a very rare entity. We report a 29 years old female patient, who was managed on 'wait and observe policy', for presumed benign intramural cyst of the esophagus for over 7 years. This resulted in dense pericystic adhesions and overlying muscular atrophy which caused difficulties during operation. Waiting for symptoms before resection leads to increased operative risk, therefore, early surgery, regardless of age, symptoms or location is strongly recommended

Duplicación quística del esófago / Cystic duplication of the esophagus

Duplication is defined as the presence of a complete or partial double structure, with a variable length. In esophagus, duplications, diverticuli and cysts might be manifestations of the same embriologic defect. The most common is the Cystic Duplication of the esophagus (CDE), which represents the esophageal duplication, either spherical or tubular, with squamous or columnar epithelium, and a double muscular layer. Clinical Case: male, 38 years old with no previous relevant data, and sudden, complete and persistent post ingestion aphagia, intense presternal pain, and a 12 Kg. weight loss in 15 days. Endoscopy showed unsurpassable stenosis of the lower third of the esophagus, with normal mucosa. Total esophagectomy and replacement with a gastric tube, was performed. He had a good postoperative course. PATHOLOGY: A total esophagectomy open specimen showing a cystic structure at the posterior wall was submitted, which showed a thick, muscular-like wall and hemorrhagic internal surface. Microscopically it had a pseudostratified columnar, ciliated epithelium, alternating with sloughed hemorrhagic areas, fibrosis and stromal siderophagi Leiomuscular double-layered wall. CDE is very infrequent, and is the second most frequent after leiomiomas as a benign esophageal mass. From 10 to 15 percent of all digestive duplications take place at the esophagus. There are different theories to explain its origin. Differential diagnosis must be made mainly with brochogenic cyst, generally anterior and with cartilage. Treatment is surgical.

Quiste de diplicación esofagica, un hallazgo infrecuente / Cyst of duplication esophagical an uncommon discovery

La duplicación esofágica es una patología congénita que puede ser quística o tubular. Se cree que entre la 5 y 8 semana embrionaria por una falla en el proceso de vacuolización para formar la luz del esófago esto da como resultado la formación de los quistes esofágicos los cuales pueden estar recubiertos de diferentes tipos de epitelio, tener contenido y calcificaciones y estar recubiertos por capas de músculo liso, que el caso específico de los quistes de origen esofágico, deben tener doble capa de músculo liso y no tener cartílago bronquiales en su interior. Son un hallazgo infrecuente y constituyen el 0,5 por ciento al 2,5 por ciento de los tumores de benignos del esófago, su localización más frecuente en 1/3 inferior del esófago en cara lateral derecha. Más comúnmente diagnosticados en niños y raros en adultos, que son frecuentemente asintomáticos y diagnosticados en forma incidental. El ultrasonido endoscópico es el método hoy, de elección diagnóstico por permitirnos precisar las características de la lesión submucosa como, capa de donde se origina, patrón de la masa, tamaño y localización exacta, presencia de cartílago, calcificaciones, etc. La cirugía es recomendada por sus posibles complicaciones durante la evolución natural de la enfermedad y para establecer diagnóstico definitivo con la pieza resecada. Muy pocos reportes hay en la literatura mundial, a nuestro entender este seria el primero reportado en Venezuela

Esophageal carcinoma originating in a duplication cyst: case report

Apresenta-se um caso de homem com 61 anos de idade, portador de carcinoma do terço médio do esôfago. Foi submetido a ressecçäo gastro-esofágica radical através de laparotomia mediana e toracotomia direita. O exame histopatológico mostrou carcinoma de células escamosas nitidamente originado da camada epitelial de cisto esofágico duplicado. Mostrou-se mediante imunohistoquímica células tumorais coradas para p53. Em 11 meses de evoluçäo o paciente permanece asssintomático